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Diabetes Research Today is a free monthly online journal that collates and summarizes the latest research about Diabetes, including details on insulin, type i, type ii, diet, treatment, prevention.


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Congenital nasal pyriform aperture stenosis with semilobar holoprosencephaly.

Chan EY, Ng DK, Chong AS, Hui Y, Fu YM

Department of Paediatrics, Kwong Wah Hospital, Waterloo Road, Hong Kong, Kowloon, Hong Kong SAR, PR China.

We describe a child who has congenital nasal pyriform aperture stenosis with single maxillary central incisor, holoprosencephaly and central diabetes insipidus without any apparent anterior pituitary dysfunction. Conservative management of the congenital nasal pyriform aperture stenosis is adopted and management of diabetes insipidus is described. A literature review is undertaken.

Published 3 January 2005 in Int J Pediatr Otorhinolaryngol, 69(1): 93-6.
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